Mouth and Teeth
Dental abnormalities are common. Individuals with MPS VI
frequently have widely spaced and poorly formed teeth.
Unerupted teeth, permanent teeth which are impacted, and
hyperplastic tooth follicles are also typical.1
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Small, Irregular, Widely
Spaced Teeth. With enlarged
tongue and lips in a 16-year-old
male with rapidly advancing
disease (left). A 6-year-old male
with more slowly advancing
disease exhibits subtle features
(right). |
| Photo courtesy of The National MPS Society, Inc. (right) |
- Smith KS, Hallett KB, Hall RK, et al. Mucopolysaccharidosis: MPS VI and associated delayed tooth
eruption. Int J Oral Maxillofac Surg. 1995;24:176-180.
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