Mouth and Teeth

Dental abnormalities are common. Individuals with MPS VI frequently have widely spaced and poorly formed teeth. Unerupted teeth, permanent teeth which are impacted, and hyperplastic tooth follicles are also typical.¹

		Small, Irregular, Widely Spaced Teeth. With enlarged tongue and lips in a 16-year-old male with rapidly advancing disease (left). A 6-year-old male with more slowly advancing disease exhibits subtle features (right).
Photo courtesy of The National MPS Society, Inc. (right)

1. Smith KS, Hallett KB, Hall RK, et al. Mucopolysaccharidosis: MPS VI and associated delayed tooth eruption. Int J Oral Maxillofac Surg. 1995;24:176-180.